Repair of total anomalous pulmonary venous return (TAPVR) with pulmonary artery (PA) Stenosis in adult

Background/Introduction Less than 7% patients with TAPVR survive into adulthood. Predictors of survive in untreated patients are: absence of concomitant CHD & atrial isomerism; large ASD; low pulmonary vascular resistance; mild/moderate TV incompetence. Experience of TAPVR repair in adults restricted by prevalence of case reports. Majority of repaired were ≥50 years old. There have been four case reports of untreated TAPVC diagnosed after 60 years of age, and three of them underwent successful surgery on 61[J Melki,1992], 63 [MH McMullan,1992] and 66 years of age[U Wetzel,2010]. Large surgical series presented by X Jian, 2012 [12 pts], S Talwar, 2008 [27 pts], B Korbmacher, 2001[12 pts] and J RodriguezCollado, 1992 [19 pts]. Among case reports of TAPVR in adults, up to our knowledge, there are only 4 patients with TAPVR and with PA valve stenosis /RVOT obstruction.